{"id":3859,"date":"2020-10-26T09:59:09","date_gmt":"2020-10-26T08:59:09","guid":{"rendered":"https:\/\/dev.retina.ch\/?post_type=netzhauterkrankungen&#038;p=3859"},"modified":"2025-03-05T15:35:16","modified_gmt":"2025-03-05T14:35:16","slug":"malattia-leventinese","status":"publish","type":"netzhauterkrankungen","link":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/malattia-leventinese\/","title":{"rendered":"Malattia Leventinese"},"content":{"rendered":"\n<p>La Malattia Leventinese (\u00e9galement appel\u00e9e \u00ab\u00a0dystrophie r\u00e9tinienne de Doyne Honeycomb\u00a0\u00bb) est une maladie d\u00e9g\u00e9n\u00e9rative h\u00e9r\u00e9ditaire de la r\u00e9tine, pr\u00e9sente dans le monde entier, mais particuli\u00e8rement fr\u00e9quente au Tessin. Les premiers sympt\u00f4mes de la maladie apparaissent entre 30 et 40 ans avec des difficult\u00e9s d&rsquo;adaptation aux diff\u00e9rences de luminosit\u00e9 et un d\u00e9clin relativement rapide de l&rsquo;acuit\u00e9 visuelle. Ces sympt\u00f4mes sont le r\u00e9sultat d&rsquo;une d\u00e9g\u00e9n\u00e9rescence pr\u00e9coce de la macula. La maladie n&rsquo;induit pas une c\u00e9cit\u00e9 compl\u00e8te, mais une d\u00e9ficience visuelle s\u00e9v\u00e8re.<\/p>\n\n\n\n<p>Les premiers signes de la maladie se reconnaissent aux d\u00e9p\u00f4ts blancs (druses) dans la zone de la macula. Ces d\u00e9p\u00f4ts deviennent de plus en plus fr\u00e9quents au fil du temps et s&rsquo;amassent pour former un seul grand d\u00e9p\u00f4t. Cela entra\u00eene la mort des cellules photosensibles (photor\u00e9cepteurs). La p\u00e9riph\u00e9rie de la r\u00e9tine reste exclue de ce processus. \u00c0 ce jour, il n&rsquo;existe aucun traitement pour la malattia leventinese.<\/p>\n\n\n\n<p>Jusqu&rsquo;\u00e0 pr\u00e9sent, un seul g\u00e8ne EMPEF1 a \u00e9t\u00e9 tenu pour responsable de la maladie. La maladie est transmise de g\u00e9n\u00e9ration en g\u00e9n\u00e9ration, avec un risque de 50 % pour les enfants d&rsquo;une personne atteinte.<\/p>\n\n\n\n<div class=\"wp-block-columns icon-block is-layout-flex wp-container-core-columns-is-layout-9d6595d7 wp-block-columns-is-layout-flex\">\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\"><span class='maxbutton-6-container mb-container'><a class=\"maxbutton-6 maxbutton maxbutton-beratung-anmelden\" title=\"Pers\u00f6nliche Beratung Anmelden\" href=\"\/beratungen\/individuelle-beratung\/\" data-maxbuttoncounter=\"{&quot;button_id&quot;:&quot;6&quot;,&quot;url&quot;:&quot;\\\/beratungen\\\/individuelle-beratung\\\/&quot;,&quot;check&quot;:&quot;bWuaKQZn&quot;}\" data-maxbuttonpage=\"{&quot;id&quot;:3859,&quot;type&quot;:&quot;netzhauterkrankungen&quot;}\"><span class=\"mb-icon\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-comments-black-400x356.png\" title=\"icon-comments-black\" width=\"400\" height=\"356\"   border=\"0\" \/><\/span><span class=\"mb-icon-hover\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img-hover\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-comments-yellow-400x356.png\" title=\"icon-comments-black\" width=\"576\" height=\"512\"   border=\"0\" \/><\/span><span class='mb-text' >S&#039;inscrire pour<\/span><span class=\"mb-text2\"  >une consultation<\/span><\/a><\/span>\n<\/div>\n\n\n\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\"><span class='maxbutton-7-container mb-container'><a class=\"maxbutton-7 maxbutton maxbutton-kontakt\" title=\"Retina Suisse Kontakt\" href=\"\/kontakt\/\" data-maxbuttoncounter=\"{&quot;button_id&quot;:&quot;7&quot;,&quot;url&quot;:&quot;\\\/kontakt\\\/&quot;,&quot;check&quot;:&quot;Ot5xIOiH&quot;}\" data-maxbuttonpage=\"{&quot;id&quot;:3859,&quot;type&quot;:&quot;netzhauterkrankungen&quot;}\"><span class=\"mb-icon\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-phone-black-400x400.png\" title=\"icon-phone-black\" width=\"400\" height=\"400\"   border=\"0\" \/><\/span><span class=\"mb-icon-hover\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img-hover\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-phone-yellow-400x400.png\" title=\"icon-phone-black\" width=\"512\" height=\"512\"   border=\"0\" \/><\/span><span class='mb-text' >Retina Suisse<\/span><span class=\"mb-text2\"  >Contact<\/span><\/a><\/span>\n<\/div>\n\n\n\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\"><span class='maxbutton-3-container mb-container'><a class=\"maxbutton-3 maxbutton maxbutton-retina-suisse-mitgliedschaft\" title=\"Retina Suisse Mitgliedschaft\" href=\"\/mitgliedschaft\/\" data-maxbuttoncounter=\"{&quot;button_id&quot;:&quot;3&quot;,&quot;url&quot;:&quot;\\\/mitgliedschaft\\\/&quot;,&quot;check&quot;:&quot;Rweb1zDP&quot;}\" data-maxbuttonpage=\"{&quot;id&quot;:3859,&quot;type&quot;:&quot;netzhauterkrankungen&quot;}\"><span class=\"mb-icon\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-users.png\" title=\"icon-users\" width=\"640\" height=\"512\"   border=\"0\" \/><\/span><span class=\"mb-icon-hover\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img-hover\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-users-yellow.png\" title=\"icon-users\" width=\"640\" height=\"512\"   border=\"0\" \/><\/span><span class='mb-text' >Adh\u00e9rer \u00e0<\/span><span class=\"mb-text2\"  >Retina Suisse<\/span><\/a><\/span>\n<\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>La Malattia leventinese (\u00e9galement appel\u00e9e \u00ab\u00a0dystrophie r\u00e9tinienne de Doyne Honeycomb\u00a0\u00bb) est une maladie d\u00e9g\u00e9n\u00e9rative h\u00e9r\u00e9ditaire de la r\u00e9tine de l&rsquo;\u0153il, pr\u00e9sente dans le monde entier, mais particuli\u00e8rement fr\u00e9quente au Tessin.<\/p>\n","protected":false},"featured_media":0,"template":"","meta":{"_acf_changed":false,"inline_featured_image":false,"_FSMCFIC_featured_image_caption":"","_FSMCFIC_featured_image_nocaption":"","_FSMCFIC_featured_image_hide":"","footnotes":"","_links_to":"","_links_to_target":""},"categories":[55],"class_list":["post-3859","netzhauterkrankungen","type-netzhauterkrankungen","status-publish","hentry","category-maladies"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Malattia Leventinese &#8226; 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