{"id":3864,"date":"2020-10-28T11:21:35","date_gmt":"2020-10-28T10:21:35","guid":{"rendered":"https:\/\/dev.retina.ch\/?post_type=netzhauterkrankungen&p=3864"},"modified":"2025-03-05T15:38:44","modified_gmt":"2025-03-05T14:38:44","slug":"morbus-best","status":"publish","type":"netzhauterkrankungen","link":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/","title":{"rendered":"Morbus Best"},"content":{"rendered":"\n

La maladie de Best (d\u00e9nomm\u00e9e aussi dystrophie maculaire vitelliforme) est tr\u00e8s souvent diagnostiqu\u00e9e d\u00e8s l’enfance du patient. L’\u00e9volution varie beaucoup de cas en cas, l’acuit\u00e9 visuelle peut \u00eatre normale ou seulement un peu r\u00e9duite. Au fur et \u00e0 mesure de la diminution de la vision, le patient est de plus en plus sensible \u00e0 l’\u00e9blouissement et des troubles de la perception des couleurs peuvent survenir. Les d\u00e9gradations du champ visuel central (scotome central) s’\u00e9tendent mais n’affectent pas la p\u00e9riph\u00e9rie de la r\u00e9tine.<\/p>\n\n\n\n

Au stade pr\u00e9coce, on distingue au centre de la r\u00e9tine une tache bomb\u00e9e jaun\u00e2tre, nettement d\u00e9limit\u00e9e, ressemblant \u00e0 un jaune d’\u0153uf au plat. A ce stade de la maladie, la vision est en r\u00e8gle g\u00e9n\u00e9rale intacte ou seulement un peu diminu\u00e9e. En d\u00e9pit de cette l\u00e9sion \u00e0 l’apparence de kyste, l’acuit\u00e9 visuelle peut encore demeurer normale, ou du moins suffisante, durant de nombreuses ann\u00e9es. Lorsque le processus d’\u00e9volution progresse, une liqu\u00e9faction de la substance jaune peut se produire (pseudo-empy\u00e8se). Dans de nombreux cas, cette mati\u00e8re d’apparence kystique se d\u00e9compose (stade vitelli\u00e9ruptif) ce qui cause une forte diminution de la capacit\u00e9 visuelle. Au stade de \u00abl’\u0153uf brouill\u00e9\u00bb, on constate de nombreux d\u00e9p\u00f4ts jaun\u00e2tres dans l’\u00e9pith\u00e9lium pigmentaire r\u00e9tinien (RPE).<\/p>\n\n\n\n

Au stade avanc\u00e9, une formation de nouveaux vaisseaux sanguins (n\u00e9ovascularisation) peut se produire dans la choro\u00efde, ce qui en r\u00e8gle g\u00e9n\u00e9rale induit une perte de vision tr\u00e8s s\u00e9v\u00e8re. La maladie de Best peut affecter les deux yeux ou un seul \u0153il.<\/p>\n\n\n\n

La maladie de Best est caus\u00e9e par un d\u00e9faut g\u00e9n\u00e9tique de type autosomique dominant. \u00c0 ce jour, il n’existe pas encore de possibilit\u00e9 de traitement sp\u00e9cifique pour cette maladie. Il est recommand\u00e9 aux patients d’avoir une alimentation saine comportant beaucoup de l\u00e9gumes verts pour leur apport en lut\u00e9ine et de porter une tr\u00e8s bonne protection contre les UV.<\/p>\n\n\n\n

Des moyens auxiliaires grossissants sont tr\u00e8s utiles pour am\u00e9liorer la capacit\u00e9 visuelle.<\/p>\n\n\n\n

\n
<\/span><\/span>S'inscrire pour<\/span>une consultation<\/span><\/a><\/span>\n<\/div>\n\n\n\n
<\/span><\/span>Retina Suisse<\/span>Contact<\/span><\/a><\/span>\n<\/div>\n\n\n\n
<\/span><\/span>Adh\u00e9rer \u00e0<\/span>Retina Suisse<\/span><\/a><\/span>\n<\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"

La maladie de Best (d\u00e9nomm\u00e9e aussi dystrophie maculaire vitelliforme) est tr\u00e8s souvent diagnostiqu\u00e9e d\u00e8s l’enfance du patient. <\/p>\n","protected":false},"featured_media":0,"template":"","meta":{"_acf_changed":false,"inline_featured_image":false,"_FSMCFIC_featured_image_caption":"","_FSMCFIC_featured_image_nocaption":"","_FSMCFIC_featured_image_hide":"","footnotes":"","_links_to":"","_links_to_target":""},"categories":[55],"class_list":["post-3864","netzhauterkrankungen","type-netzhauterkrankungen","status-publish","hentry","category-maladies"],"acf":[],"yoast_head":"\nMorbus Best • vitelliforme • dystrophie maculaire eidot\u00e9rique Retina Suisse<\/title>\n<meta name=\"description\" content=\"Perte pr\u00e9coce de la vision, sensibilit\u00e9 \u00e0 la lumi\u00e8re et troubles de la vision des couleurs - la vision centrale diminue, la vision p\u00e9riph\u00e9rique demeure.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Morbus Best • vitelliforme • dystrophie maculaire eidot\u00e9rique Retina Suisse\" \/>\n<meta property=\"og:description\" content=\"Perte pr\u00e9coce de la vision, sensibilit\u00e9 \u00e0 la lumi\u00e8re et troubles de la vision des couleurs - la vision centrale diminue, la vision p\u00e9riph\u00e9rique demeure.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/\" \/>\n<meta property=\"og:site_name\" content=\"Retina Suisse\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/retinasuisse\/\" \/>\n<meta property=\"article:modified_time\" content=\"2025-03-05T14:38:44+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Dur\u00e9e de lecture estim\u00e9e\" \/>\n\t<meta name=\"twitter:data1\" content=\"2 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/\",\"url\":\"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/\",\"name\":\"Morbus Best • vitelliforme • dystrophie maculaire eidot\u00e9rique Retina Suisse\",\"isPartOf\":{\"@id\":\"https:\/\/retina.ch\/fr\/#website\"},\"datePublished\":\"2020-10-28T10:21:35+00:00\",\"dateModified\":\"2025-03-05T14:38:44+00:00\",\"description\":\"Perte pr\u00e9coce de la vision, sensibilit\u00e9 \u00e0 la lumi\u00e8re et troubles de la vision des couleurs - la vision centrale diminue, la vision p\u00e9riph\u00e9rique demeure.\",\"breadcrumb\":{\"@id\":\"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/#breadcrumb\"},\"inLanguage\":\"fr-FR\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Retina Suisse\",\"item\":\"https:\/\/retina.ch\/fr\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Morbus Best\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/retina.ch\/fr\/#website\",\"url\":\"https:\/\/retina.ch\/fr\/\",\"name\":\"Retina Suisse\",\"description\":\"Retina Suisse ist die Vereinigung von Patientinnen und Patienten mit Retinitis pigmentosa (RP), Makuladegeneration, Usher-Syndrom und anderen Erkrankungen des Augenhintergrundes.\",\"publisher\":{\"@id\":\"https:\/\/retina.ch\/fr\/#organization\"},\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/retina.ch\/fr\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"fr-FR\"},{\"@type\":\"Organization\",\"@id\":\"https:\/\/retina.ch\/fr\/#organization\",\"name\":\"Retina Suisse\",\"url\":\"https:\/\/retina.ch\/fr\/\",\"logo\":{\"@type\":\"ImageObject\",\"inLanguage\":\"fr-FR\",\"@id\":\"https:\/\/retina.ch\/fr\/#\/schema\/logo\/image\/\",\"url\":\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/09\/retina-auge-typo.svg\",\"contentUrl\":\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/09\/retina-auge-typo.svg\",\"width\":\"1024\",\"height\":\"1024\",\"caption\":\"Retina Suisse\"},\"image\":{\"@id\":\"https:\/\/retina.ch\/fr\/#\/schema\/logo\/image\/\"},\"sameAs\":[\"https:\/\/www.facebook.com\/retinasuisse\/\"]}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Morbus Best • vitelliforme • dystrophie maculaire eidot\u00e9rique Retina Suisse","description":"Perte pr\u00e9coce de la vision, sensibilit\u00e9 \u00e0 la lumi\u00e8re et troubles de la vision des couleurs - la vision centrale diminue, la vision p\u00e9riph\u00e9rique demeure.","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/","og_locale":"fr_FR","og_type":"article","og_title":"Morbus Best • vitelliforme • dystrophie maculaire eidot\u00e9rique Retina Suisse","og_description":"Perte pr\u00e9coce de la vision, sensibilit\u00e9 \u00e0 la lumi\u00e8re et troubles de la vision des couleurs - la vision centrale diminue, la vision p\u00e9riph\u00e9rique demeure.","og_url":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/","og_site_name":"Retina Suisse","article_publisher":"https:\/\/www.facebook.com\/retinasuisse\/","article_modified_time":"2025-03-05T14:38:44+00:00","twitter_card":"summary_large_image","twitter_misc":{"Dur\u00e9e de lecture estim\u00e9e":"2 minutes"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"WebPage","@id":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/","url":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/","name":"Morbus Best • vitelliforme • dystrophie maculaire eidot\u00e9rique Retina Suisse","isPartOf":{"@id":"https:\/\/retina.ch\/fr\/#website"},"datePublished":"2020-10-28T10:21:35+00:00","dateModified":"2025-03-05T14:38:44+00:00","description":"Perte pr\u00e9coce de la vision, sensibilit\u00e9 \u00e0 la lumi\u00e8re et troubles de la vision des couleurs - la vision centrale diminue, la vision p\u00e9riph\u00e9rique demeure.","breadcrumb":{"@id":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/#breadcrumb"},"inLanguage":"fr-FR","potentialAction":[{"@type":"ReadAction","target":["https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/"]}]},{"@type":"BreadcrumbList","@id":"https:\/\/retina.ch\/fr\/degenerescences-retiniennes\/morbus-best\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Retina Suisse","item":"https:\/\/retina.ch\/fr\/"},{"@type":"ListItem","position":2,"name":"Morbus Best"}]},{"@type":"WebSite","@id":"https:\/\/retina.ch\/fr\/#website","url":"https:\/\/retina.ch\/fr\/","name":"Retina Suisse","description":"Retina Suisse ist die Vereinigung von Patientinnen und Patienten mit Retinitis pigmentosa (RP), Makuladegeneration, Usher-Syndrom und anderen Erkrankungen des Augenhintergrundes.","publisher":{"@id":"https:\/\/retina.ch\/fr\/#organization"},"potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/retina.ch\/fr\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"fr-FR"},{"@type":"Organization","@id":"https:\/\/retina.ch\/fr\/#organization","name":"Retina Suisse","url":"https:\/\/retina.ch\/fr\/","logo":{"@type":"ImageObject","inLanguage":"fr-FR","@id":"https:\/\/retina.ch\/fr\/#\/schema\/logo\/image\/","url":"https:\/\/retina.ch\/wp-content\/uploads\/2020\/09\/retina-auge-typo.svg","contentUrl":"https:\/\/retina.ch\/wp-content\/uploads\/2020\/09\/retina-auge-typo.svg","width":"1024","height":"1024","caption":"Retina Suisse"},"image":{"@id":"https:\/\/retina.ch\/fr\/#\/schema\/logo\/image\/"},"sameAs":["https:\/\/www.facebook.com\/retinasuisse\/"]}]}},"_links":{"self":[{"href":"https:\/\/retina.ch\/fr\/wp-json\/wp\/v2\/netzhauterkrankungen\/3864","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/retina.ch\/fr\/wp-json\/wp\/v2\/netzhauterkrankungen"}],"about":[{"href":"https:\/\/retina.ch\/fr\/wp-json\/wp\/v2\/types\/netzhauterkrankungen"}],"version-history":[{"count":1,"href":"https:\/\/retina.ch\/fr\/wp-json\/wp\/v2\/netzhauterkrankungen\/3864\/revisions"}],"predecessor-version":[{"id":10527,"href":"https:\/\/retina.ch\/fr\/wp-json\/wp\/v2\/netzhauterkrankungen\/3864\/revisions\/10527"}],"wp:attachment":[{"href":"https:\/\/retina.ch\/fr\/wp-json\/wp\/v2\/media?parent=3864"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/retina.ch\/fr\/wp-json\/wp\/v2\/categories?post=3864"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}