{"id":3920,"date":"2020-10-28T11:32:25","date_gmt":"2020-10-28T10:32:25","guid":{"rendered":"https:\/\/dev.retina.ch\/?post_type=netzhauterkrankungen&#038;p=3920"},"modified":"2025-03-19T14:16:59","modified_gmt":"2025-03-19T13:16:59","slug":"sindrome-di-senior-loken","status":"publish","type":"netzhauterkrankungen","link":"https:\/\/retina.ch\/it\/malattie-della-retina\/sindrome-di-senior-loken\/","title":{"rendered":"Sindrome di Senior-Loken"},"content":{"rendered":"\n<p>La neuropatia ottica ereditaria di Leber (LHON) \u00e8 una malattia ereditaria che porta alla improvvisa perdita della vista in giovani adulti. I maschi sono pi\u00f9 soggetti delle femmine. La LHON \u00e8 causata da mutazioni del DNA contenuto nei mitocondri. I mitocondri sono degli organelli presenti nel citoplasma delle cellule. I mitocondri sono capaci di trasformare l\u2019energia presente nel cibo in energia utilizzabile dalla cellula e necessaria per lo svolgimento delle sue funzioni.<\/p>\n\n\n\n<p>I nostri occhi sono dei gran consumatori di energia e la carenza di mitocondri funzionanti porta alla perdita delle cellule gangliari della retina, quelle che convogliano i segnali dalla retina al cervello attraverso i loro prolungamenti che formano il nervo ottico. La degenerazione delle cellule gangliari porta alla degenerazione del nervo ottico e alla perdita della vista. E\u2019 importante tuttavia ricordare che la maggior parte delle persone con l\u2019alterazione genetica che causa la LHON non avr\u00e0 disturbi visivi.<\/p>\n\n\n\n<p>La LHON non causa dolore, ma \u00e8 particolarmente allarmante perch\u00e9 la persona perde all\u2019improvviso la visione centrale e la visione peggiora rapidamente lasciando solo la visione periferica. &nbsp;Ci\u00f2 significa che la maggior parte delle persone con la LHON mantiene una certa indipendenza anche se non pu\u00f2 avere una visione distinta.<\/p>\n\n\n\n<div class=\"wp-block-columns icon-block is-layout-flex wp-container-core-columns-is-layout-9d6595d7 wp-block-columns-is-layout-flex\">\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\"><span class='maxbutton-6-container mb-container'><a class=\"maxbutton-6 maxbutton maxbutton-beratung-anmelden\" title=\"Pers\u00f6nliche Beratung Anmelden\" href=\"\/beratungen\/individuelle-beratung\/\" data-maxbuttoncounter=\"{&quot;button_id&quot;:&quot;6&quot;,&quot;url&quot;:&quot;\\\/beratungen\\\/individuelle-beratung\\\/&quot;,&quot;check&quot;:&quot;bWuaKQZn&quot;}\" data-maxbuttonpage=\"{&quot;id&quot;:3920,&quot;type&quot;:&quot;netzhauterkrankungen&quot;}\"><span class=\"mb-icon\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-comments-black-400x356.png\" title=\"icon-comments-black\" width=\"400\" height=\"356\"   border=\"0\" \/><\/span><span class=\"mb-icon-hover\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img-hover\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-comments-yellow-400x356.png\" title=\"icon-comments-black\" width=\"576\" height=\"512\"   border=\"0\" \/><\/span><span class='mb-text' >Annunciarsi per<\/span><span class=\"mb-text2\"  >una consulenza<\/span><\/a><\/span>\n<\/div>\n\n\n\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\"><span class='maxbutton-7-container mb-container'><a class=\"maxbutton-7 maxbutton maxbutton-kontakt\" title=\"Retina Suisse Kontakt\" href=\"\/kontakt\/\" data-maxbuttoncounter=\"{&quot;button_id&quot;:&quot;7&quot;,&quot;url&quot;:&quot;\\\/kontakt\\\/&quot;,&quot;check&quot;:&quot;Ot5xIOiH&quot;}\" data-maxbuttonpage=\"{&quot;id&quot;:3920,&quot;type&quot;:&quot;netzhauterkrankungen&quot;}\"><span class=\"mb-icon\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-phone-black-400x400.png\" title=\"icon-phone-black\" width=\"400\" height=\"400\"   border=\"0\" \/><\/span><span class=\"mb-icon-hover\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img-hover\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-phone-yellow-400x400.png\" title=\"icon-phone-black\" width=\"512\" height=\"512\"   border=\"0\" \/><\/span><span class='mb-text' >Retina Suisse<\/span><span class=\"mb-text2\"  >Contatto<\/span><\/a><\/span>\n<\/div>\n\n\n\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\"><span class='maxbutton-3-container mb-container'><a class=\"maxbutton-3 maxbutton maxbutton-retina-suisse-mitgliedschaft\" title=\"Retina Suisse Mitgliedschaft\" href=\"\/mitgliedschaft\/\" data-maxbuttoncounter=\"{&quot;button_id&quot;:&quot;3&quot;,&quot;url&quot;:&quot;\\\/mitgliedschaft\\\/&quot;,&quot;check&quot;:&quot;Rweb1zDP&quot;}\" data-maxbuttonpage=\"{&quot;id&quot;:3920,&quot;type&quot;:&quot;netzhauterkrankungen&quot;}\"><span class=\"mb-icon\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-users.png\" title=\"icon-users\" width=\"640\" height=\"512\"   border=\"0\" \/><\/span><span class=\"mb-icon-hover\"><img loading=\"lazy\" decoding=\"async\" class=\"mb-img-hover\" src=\"https:\/\/retina.ch\/wp-content\/uploads\/2020\/10\/icon-users-yellow.png\" title=\"icon-users\" width=\"640\" height=\"512\"   border=\"0\" \/><\/span><span class='mb-text' >Iscrizione<\/span><span class=\"mb-text2\"  >Retina Suisse<\/span><\/a><\/span>\n<\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>La neuropatia ottica ereditaria di Leber (LHON) \u00e8 una malattia ereditaria che porta alla improvvisa perdita della vista in giovani adulti. <\/p>\n","protected":false},"featured_media":0,"template":"","meta":{"_acf_changed":false,"inline_featured_image":false,"_FSMCFIC_featured_image_caption":"","_FSMCFIC_featured_image_nocaption":"","_FSMCFIC_featured_image_hide":"","footnotes":"","_links_to":"","_links_to_target":""},"categories":[56],"class_list":["post-3920","netzhauterkrankungen","type-netzhauterkrankungen","status-publish","hentry","category-malattie"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Sindrome di Senior-Loken &#8226; 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